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Information about Pityriasis Rubra Pilaris

Pityriasis rubra pilaris
Classification & external resources
ICD-10L44.0
ICD-9696.4
OMIM173200
DiseasesDB29305
MedlinePlus001471
eMedicinederm/337 
MeSHD010916
Pityriasis rubra pilaris (PRP) is a rare and chronic skin disorder that often has a sudden onset. Symptoms may include reddish-orange patches (Latin: rubra) on the skin, severe flaking (Latin: pityriasis), uncomfortable itching, thickening of the skin on the feet and hands, and thickened bumps around hair follicles (Latin: pilus for hair). For some, early symptoms may also include generalized swelling of the legs, feet and other parts of the body. PRP has a varied clinical progression and a varied rate of improvement. There is no known cause or cure.

It was first described by Marie-Guillaume-Alphonse Devergie in 1856,[1] and the condition is also known as Devergie's disease.[2]

Classification

Dr. W.A.D. Griffiths, from Great Britain, classified six forms of PRP in the early 1980s.[3] At this time, the causes of PRP are still unknown and symptoms can be difficult to diagnose. Frequently, more than one medical professional will be consulted before an accurate PRP diagnosis is made.

Dermatologists have identified both an acquired form and an inherited form (familial) of PRP and have described them in medical journals. The acquired form usually shows a spontaneous or gradual remission of symptoms within several years although long-term symptoms may continue for years. The inherited form starts early in childhood with persistent long-term symptoms into adulthood.

Although most people who develop PRP are over age 50, individuals of any age, race, and nationality can be affected. Women and men seem to be equally affected.

Footnotes

1. ^ Devergie M. G. A. (1856). "[Pityriasis pilaris, a skin disease not described by dermatologists] (Pityriasis pilaris, maladie de la peau non décrite par les dermatologistes)." (in French). Gazette hebdomadaire de médecine et de chirurgie, Paris 3: 197-201. 
2. ^ M. G. A. Devergie and the eponymous named Devergie's disease at Who Named It
3. ^ Pityriasis rubra pilaris. DermNZ (New Zealand Dermatological Society) (26 Dec 2006). Retrieved on 2007-05-08. - describes the various forms

External links

  • PRP Support Group - information regarding day-to-day care and medical treatment and having an international membership.
  • Dr. Griffith (June 1998). in Editors Champion R.H., Burton J.L., Burns D.A. and Breathnach S.M.: Textbook of Dermatology, 6th edition, 1539–1545. ISBN 0632050640. 
 •  • [ e]
Diseases of the skin and subcutaneous tissue (integumentary system) (, )
InfectionsStaphylococcus (Staphylococcal scalded skin syndrome, Impetigo, Boil, Carbuncle) - Cellulitis - Acute lymphadenitis - Pilonidal cyst - Corynebacterium (Erythrasma)
Bullous disordersPemphigus - Pemphigoid (Bullous pemphigoid) - Dermatitis herpetiformis
Dermatitis and eczemaAtopic dermatitis - Seborrhoeic dermatitis (Dandruff, Cradle cap) - Diaper rash - Urushiol-induced contact dermatitis - Contact dermatitis - Erythroderma - Lichen simplex chronicus - Prurigo nodularis - Itch - Pruritus ani - Nummular dermatitis - Dyshidrosis - Pityriasis alba
Papulosquamous disordersPsoriasis (Psoriatic arthritis) - Parapsoriasis (Pityriasis lichenoides et varioliformis acuta, Pityriasis lichenoides chronica) - Pityriasis rosea - Lichen planus - Pityriasis rubra pilaris
Urticaria and erythemaUrticaria (Dermatographic urticaria, Cholinergic urticaria) - Erythema (Erythema multiforme, Stevens-Johnson syndrome, Toxic epidermal necrolysis, Erythema nodosum, Erythema annulare centrifugum, Erythema marginatum)
Radiation-related disordersSunburn - Actinic keratosis - Polymorphous light eruption - Radiodermatitis - Erythema ab igne
Disorders of skin appendagesNail disease - Alopecia areata - Telogen effluvium - Lichen planus - Hypertrichosis (Hirsutism) - Acne vulgaris - Rosacea (Rhinophyma) - Pseudofolliculitis barbae - Hidradenitis suppurativa - Miliaria - Anhidrosis - Body odor
Otherpigmentation (Vitiligo, Melasma, Freckle, Caf au lait spot, Lentigo/Liver spot) - Seborrheic keratosis - Acanthosis nigricans - Callus - Pyoderma gangrenosum - Bedsore - Keloid - Granuloma annulare - Necrobiosis lipoidica - Granuloma faciale - Lupus erythematosus - Morphea - Calcinosis cutis - Sclerodactyly - Ainhum - Livedoid vasculitis
see also (Q80-Q84, )
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The International Statistical Classification of Diseases and Related Health Problems (most commonly known by the abbreviation ICD
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List of ICD-10 codes. The version for 2007 is available online at [1]

Chapter Blocks Title
I Certain infectious and parasitic diseases
II Neoplasms
III Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
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The International Statistical Classification of Diseases and Related Health Problems (most commonly known by the abbreviation ICD
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The following is a list of codes for International Statistical Classification of Diseases and Related Health Problems. These codes are in the public domain.

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This is a list of diseases of the skin.
  • Acne
  • Actinic keratosis
  • Angioma
  • Athlete's foot
  • Aquagenic pruritus
  • Argyria
  • Atopic dermatitis
  • Baldness
  • Basal cell carcinoma
  • Bed sore
  • Behcet's disease
  • Blepharitis
  • Boil

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Pityriasis commonly refers to flaking of the skin. Types include:
  • Pityriasis alba
  • Pityriasis lichenoides chronica
  • Pityriasis lichenoides et varioliformis acuta
  • Pityriasis rosea
  • Pityriasis rubra pilaris
  • Pityriasis versicolor

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A hair follicle is part of the skin that grows hair by packing old cells together. Attached to the follicle is a sebaceous gland, a tiny sebum-producing gland found everywhere except on the palms, lips and soles of the feet.
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Marie-Guillaume-Alphonse Devergie (February 15, 1798 - October 2, 1879) was a French dermatologist who was born in Paris. In 1834 he became a physician of Parisian hospitals (Médecin des Hôpitaux de Paris), and in 1840 succeeded Laurent-Théodore Biett (1781-1840) at the Hôpital
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A genetic disorder is a condition caused by abnormalities in genes or chromosomes. While some diseases, such as cancer, are due to genetic abnormalities acquired in a few cells during life, the term "genetic disease" most commonly refers to diseases present in all cells of the body
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Who Named It? is an English-language dictionary of medical eponyms and the people associated with their identification. Though this is a dictionary, many eponyms and persons are presented in extensive articles with comprehensive bibliographies.
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Skin layers: epidermis, dermis, and subcutis, showing a hair follicle, sweat gland & sebaceous gland.]] In zootomy and dermatology, skin is the largest organ of the integumentary system made up of multiple layers of epithelial tissues that guard underlying muscles and organs.
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subcutis is the layer of tissue directly underlying the cutis. It is mainly composed of adipose tissue. Its physiological function includes insulation and storage of nutrients.

Subcutaneous injections are given by injecting a fluid or a solid pellet into the subcutis.
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In zootomy, the integumentary system is the external covering of the body, comprising the skin, hair, feathers, scales, nails, sweat glands and their products (sweat and mucus).
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Staphylococcus
Rosenbach 1884

Species

S. afermentans
S. aureus
S. auricularis
S. capitis
S. caprae
S. cohnii
S. epidermidis
S. felis
S.
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MeSH D013206 Staphylococcal scalded skin syndrome, SSSS, also known as Pemphigus neonatorum or Ritter's disease, is a dermatological condition caused by Staphylococcus aureus.
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Impetigo
Classification & external resources

Skin lesions that proved to be impetigo.
ICD-10 L 01.
ICD-9 684

DiseasesDB 6753
MedlinePlus 000860
eMedicine derm/195   emerg/283 med/1163 ped/1172 Impetigo
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Boil
Classification & external resources

ICD-10 L 02.
ICD-9 680.9

DiseasesDB 29434

MeSH D005667 Boil or furuncle is a skin disease caused by the inflammation of hair follicles, thus resulting in the localized accumulation of
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MeSH D002481 Cellulitis is an inflammation of the connective tissue underlying the skin, that can be caused by a bacterial infection. Cellulitis can be caused by normal skin flora or by exogenous bacteria, and often occurs where the skin has previously been broken: cracks in
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Lymphadenopathy
Classifications and external resources

ICD-10 I 88. , L 04. , R 59.1
ICD-9 289.1 - 289.3 , 683 , 785.6

DiseasesDB 22225

eMedicine ped/1333  
MeSH D008206 Lymphadenopathy
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MeSH D010864 A pilonidal cyst (from Latin meaning 'hair nest') is a blanket term for any type of skin infection near the tailbone. The term "pilonidal cyst" can be misleading, as a majority of the time, this is actually an abscess.
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Corynebacteriaceae

Genus: Corynebacterium
Lehmann & Neumann 1896

Species

See text.
Corynebacterium is a genus of Gram-positive, facultatively anaerobic, non-motile, rod-shaped actinobacteria.
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Erythrasma
Classification & external resources

ICD-10 L 08.1
ICD-9 039.0

DiseasesDB 29630
MedlinePlus 001470
eMedicine derm/140  
MeSH D004894 Erythrasma
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Blister
Classification & external resources

ICD-10 T14.0
ICD-9 910 - 914 , 940.0 - 949.5

A blister or bulla is a defense mechanism of the human body.
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